The association between environmental events and self-injurious behaviour in Cornelia de Lange syndrome

Joanna Moss, Christopher Oliver, S Hall, K Arron, J Sloneem, J Petty

Research output: Contribution to journalArticle

34 Citations (Scopus)


BACKGROUND: There has been limited empirical research into the environmental causes of self-injury in Cornelia de Lange syndrome. The present study examined the variability of self-injurious behaviour in Cornelia de Lange syndrome across environmental setting events. Additionally, the association between setting events and more specific environmental events was examined. METHOD: A descriptive analysis of observational data on eight children with Cornelia de Lange syndrome aged between 4 and 14 years was carried out. The association between self-injurious behaviour and four environmental setting events and between specific environmental events and setting events was examined using established statistical methods for observational data. RESULTS: Seven out of eight of the participants showed at least one form of self-injurious behaviour that was associated with a particular setting event. The study also demonstrated that the relationship between setting events and environmental events is extremely variable across individuals. CONCLUSIONS: Self-injurious behaviour in some individuals with Cornelia de Lange syndrome is associated with environmental events although the precise nature of the association warrants clarification. Using broad setting events as a methodological tool in isolation provides some insight into the role of specific environmental factors in maintaining self-injurious behaviour but the integrity of setting events must be established.
Original languageEnglish
Pages (from-to)269-277
Number of pages9
JournalJournal of Intellectual Disability Research
Publication statusPublished - 1 Apr 2005


  • descriptive analysis
  • Cornelia de Lange syndrome
  • self-injurious behaviour


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