Contrasting profiles of everyday executive function in Smith-Magenis syndrome and down syndrome

Research output: Contribution to journalArticle

Colleges, School and Institutes

Abstract

Everyday executive function (EF) was examined in Smith–Magenis syndrome (SMS), associated with high risk of behaviour disorder, and Down syndrome (DS), associated with relatively low risk of behaviour disorder. Caregivers of 13 children with SMS and 17 with DS rated everyday EF using the Behavioral Rating Inventory of Executive Functioning-Preschool. Greater everyday EF deficits relative to adaptive ability were evident in SMS than in DS. The SMS profile of everyday EF abilities was relatively uniform; in DS emotional control strengths and working memory weaknesses were evident. Findings implicate broad everyday EF difficulties in SMS compared to DS, corresponding with increased rates of behaviour disorder in SMS. Findings further suggest that everyday EF profiles may, in part, be syndrome related.

Details

Original languageEnglish
JournalJournal of Autism and Developmental Disorders
Early online date12 May 2017
Publication statusE-pub ahead of print - 12 May 2017

Keywords

  • Smith–Magenis syndrome, Down syndrome, Executive function, BRIEF-P