Brief Report: Repetitive Behaviour Profiles in Williams syndrome: Cross Syndrome Comparisons with Prader-Willi and Down syndromes

Research output: Contribution to journalArticle

Standard

Harvard

APA

Vancouver

Author

Bibtex

@article{bb47770a9d6942298cb01675a779caa2,
title = "Brief Report: Repetitive Behaviour Profiles in Williams syndrome:: Cross Syndrome Comparisons with Prader-Willi and Down syndromes",
abstract = "This study describes the profile of repetitive behaviour in individuals with Williams syndrome, utilising cross-syndrome comparisons with people with Prader-Willi and Down syndromes. The Repetitive Behaviour Questionnaire was administered to caregivers of adults with Williams (n = 96), Prader-Willi (n = 103) and Down (n = 78) syndromes. There were few group differences, although participants with Williams syndrome were more likely to show body stereotypies. Individuals with Williams syndrome also showed more hoarding and less tidying behaviours than those with Down syndrome. IQ and adaptive ability were negatively associated with repetitive questioning in people with Williams syndrome. The profile of repetitive behaviour amongst individuals with Williams syndrome was similar to the comparison syndromes. The cognitive mechanisms underlying these behaviours in genetic syndromes warrant further investigation.",
keywords = "Williams syndrome , Prader-Willi syndrome , Down syndrome , repetitive behaviour",
author = "R. Royston and C. Oliver and J. Moss and D. Adams and K. Berg and C. Burbidge and P. Howlin and L. Nelson and C. Stinton and Jane Waite",
year = "2017",
month = "10",
day = "4",
doi = "10.1007/s10803-017-3319-6",
language = "English",
journal = "Journal of Autism and Developmental Disorders",
issn = "0162-3257",
publisher = "Springer",

}

RIS

TY - JOUR

T1 - Brief Report: Repetitive Behaviour Profiles in Williams syndrome:

T2 - Cross Syndrome Comparisons with Prader-Willi and Down syndromes

AU - Royston, R.

AU - Oliver, C.

AU - Moss, J.

AU - Adams, D.

AU - Berg, K.

AU - Burbidge, C.

AU - Howlin, P.

AU - Nelson, L.

AU - Stinton, C.

AU - Waite, Jane

PY - 2017/10/4

Y1 - 2017/10/4

N2 - This study describes the profile of repetitive behaviour in individuals with Williams syndrome, utilising cross-syndrome comparisons with people with Prader-Willi and Down syndromes. The Repetitive Behaviour Questionnaire was administered to caregivers of adults with Williams (n = 96), Prader-Willi (n = 103) and Down (n = 78) syndromes. There were few group differences, although participants with Williams syndrome were more likely to show body stereotypies. Individuals with Williams syndrome also showed more hoarding and less tidying behaviours than those with Down syndrome. IQ and adaptive ability were negatively associated with repetitive questioning in people with Williams syndrome. The profile of repetitive behaviour amongst individuals with Williams syndrome was similar to the comparison syndromes. The cognitive mechanisms underlying these behaviours in genetic syndromes warrant further investigation.

AB - This study describes the profile of repetitive behaviour in individuals with Williams syndrome, utilising cross-syndrome comparisons with people with Prader-Willi and Down syndromes. The Repetitive Behaviour Questionnaire was administered to caregivers of adults with Williams (n = 96), Prader-Willi (n = 103) and Down (n = 78) syndromes. There were few group differences, although participants with Williams syndrome were more likely to show body stereotypies. Individuals with Williams syndrome also showed more hoarding and less tidying behaviours than those with Down syndrome. IQ and adaptive ability were negatively associated with repetitive questioning in people with Williams syndrome. The profile of repetitive behaviour amongst individuals with Williams syndrome was similar to the comparison syndromes. The cognitive mechanisms underlying these behaviours in genetic syndromes warrant further investigation.

KW - Williams syndrome

KW - Prader-Willi syndrome

KW - Down syndrome

KW - repetitive behaviour

U2 - 10.1007/s10803-017-3319-6

DO - 10.1007/s10803-017-3319-6

M3 - Article

JO - Journal of Autism and Developmental Disorders

JF - Journal of Autism and Developmental Disorders

SN - 0162-3257

ER -