Brief Report: Repetitive Behaviour Profiles in Williams syndrome: Cross Syndrome Comparisons with Prader-Willi and Down syndromes

Research output: Contribution to journalArticle

Authors

  • R. Royston
  • C. Oliver
  • D. Adams
  • C. Burbidge
  • P. Howlin
  • L. Nelson

Colleges, School and Institutes

External organisations

  • King's College London
  • Griffith University
  • University of East London
  • Coventry and Warwickshire Partnership NHS Trust, Coventry, United Kingdom.
  • University of Sydney
  • University of Warwick

Abstract

This study describes the profile of repetitive behaviour in individuals with Williams syndrome, utilising cross-syndrome comparisons with people with Prader-Willi and Down syndromes. The Repetitive Behaviour Questionnaire was administered to caregivers of adults with Williams (n = 96), Prader-Willi (n = 103) and Down (n = 78) syndromes. There were few group differences, although participants with Williams syndrome were more likely to show body stereotypies. Individuals with Williams syndrome also showed more hoarding and less tidying behaviours than those with Down syndrome. IQ and adaptive ability were negatively associated with repetitive questioning in people with Williams syndrome. The profile of repetitive behaviour amongst individuals with Williams syndrome was similar to the comparison syndromes. The cognitive mechanisms underlying these behaviours in genetic syndromes warrant further investigation.

Details

Original languageEnglish
JournalJournal of Autism and Developmental Disorders
Publication statusPublished - 4 Oct 2017

Keywords

  • Williams syndrome , Prader-Willi syndrome , Down syndrome , repetitive behaviour