A new, low-volume protein substitute for teenagers and adults with phenylketonuria

Research output: Contribution to journalArticle

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A new, low-volume protein substitute for teenagers and adults with phenylketonuria. / MacDonald, Anita; Lillsum, M; Cochrane, B; Davies, PH; Daly, A; Asplin, D; Hall, Susan; Cousins, A; Chakrapani, A; Robinson, P; Lee, P.

In: Journal of Inherited Metabolic Disease, Vol. 27, 01.01.2004, p. 127-135.

Research output: Contribution to journalArticle

Harvard

MacDonald, A, Lillsum, M, Cochrane, B, Davies, PH, Daly, A, Asplin, D, Hall, S, Cousins, A, Chakrapani, A, Robinson, P & Lee, P 2004, 'A new, low-volume protein substitute for teenagers and adults with phenylketonuria', Journal of Inherited Metabolic Disease, vol. 27, pp. 127-135. https://doi.org/10.1023/B:BOLI.0000028784.11080.9b

APA

MacDonald, A., Lillsum, M., Cochrane, B., Davies, PH., Daly, A., Asplin, D., Hall, S., Cousins, A., Chakrapani, A., Robinson, P., & Lee, P. (2004). A new, low-volume protein substitute for teenagers and adults with phenylketonuria. Journal of Inherited Metabolic Disease, 27, 127-135. https://doi.org/10.1023/B:BOLI.0000028784.11080.9b

Vancouver

Author

MacDonald, Anita ; Lillsum, M ; Cochrane, B ; Davies, PH ; Daly, A ; Asplin, D ; Hall, Susan ; Cousins, A ; Chakrapani, A ; Robinson, P ; Lee, P. / A new, low-volume protein substitute for teenagers and adults with phenylketonuria. In: Journal of Inherited Metabolic Disease. 2004 ; Vol. 27. pp. 127-135.

Bibtex

@article{e2b68dd2f83b415b8b4b3385e7acc582,
title = "A new, low-volume protein substitute for teenagers and adults with phenylketonuria",
abstract = "Some older patients with phenylketonuria (PKU) fail to consume their protein substitute (with or without vitamin and mineral supplements) in prescribed amounts, which contributes to poor blood phenylalanine control. PKU Express (Vitaflo), is a new low-volume (amino acids 72 g/100 g), low-carbohydrate, phenylalanine-free protein substitute with added vitamins and minerals designed for people with PKU over 8 years of age. In an open intervention study, the aim was to investigate its acceptability and effectiveness in a group of teenagers and adults with PKU. Twenty-three subjects (15 female; 8 male) with PKU, who had a median age of 17 years (range 8-37 years) took the substitute for 8 weeks. A 3-day prospective diet diary, height, weight, plasma amino acids, biochemical and haematological nutritional analytes were measured at weeks 0 and 8. Skin-puncture bloods for plasma phenylalanine were collected every 2 weeks. The median weight of protein substitute (with or without vitamin and mineral supplements) consumed decreased by 33% from 150 g (range 140-180) daily to 100 g (range 100-125) daily ( p ",
author = "Anita MacDonald and M Lillsum and B Cochrane and PH Davies and A Daly and D Asplin and Susan Hall and A Cousins and A Chakrapani and P Robinson and P Lee",
year = "2004",
month = jan,
day = "1",
doi = "10.1023/B:BOLI.0000028784.11080.9b",
language = "English",
volume = "27",
pages = "127--135",
journal = "Journal of Inherited Metabolic Disease",
issn = "0141-8955",
publisher = "Springer",

}

RIS

TY - JOUR

T1 - A new, low-volume protein substitute for teenagers and adults with phenylketonuria

AU - MacDonald, Anita

AU - Lillsum, M

AU - Cochrane, B

AU - Davies, PH

AU - Daly, A

AU - Asplin, D

AU - Hall, Susan

AU - Cousins, A

AU - Chakrapani, A

AU - Robinson, P

AU - Lee, P

PY - 2004/1/1

Y1 - 2004/1/1

N2 - Some older patients with phenylketonuria (PKU) fail to consume their protein substitute (with or without vitamin and mineral supplements) in prescribed amounts, which contributes to poor blood phenylalanine control. PKU Express (Vitaflo), is a new low-volume (amino acids 72 g/100 g), low-carbohydrate, phenylalanine-free protein substitute with added vitamins and minerals designed for people with PKU over 8 years of age. In an open intervention study, the aim was to investigate its acceptability and effectiveness in a group of teenagers and adults with PKU. Twenty-three subjects (15 female; 8 male) with PKU, who had a median age of 17 years (range 8-37 years) took the substitute for 8 weeks. A 3-day prospective diet diary, height, weight, plasma amino acids, biochemical and haematological nutritional analytes were measured at weeks 0 and 8. Skin-puncture bloods for plasma phenylalanine were collected every 2 weeks. The median weight of protein substitute (with or without vitamin and mineral supplements) consumed decreased by 33% from 150 g (range 140-180) daily to 100 g (range 100-125) daily ( p

AB - Some older patients with phenylketonuria (PKU) fail to consume their protein substitute (with or without vitamin and mineral supplements) in prescribed amounts, which contributes to poor blood phenylalanine control. PKU Express (Vitaflo), is a new low-volume (amino acids 72 g/100 g), low-carbohydrate, phenylalanine-free protein substitute with added vitamins and minerals designed for people with PKU over 8 years of age. In an open intervention study, the aim was to investigate its acceptability and effectiveness in a group of teenagers and adults with PKU. Twenty-three subjects (15 female; 8 male) with PKU, who had a median age of 17 years (range 8-37 years) took the substitute for 8 weeks. A 3-day prospective diet diary, height, weight, plasma amino acids, biochemical and haematological nutritional analytes were measured at weeks 0 and 8. Skin-puncture bloods for plasma phenylalanine were collected every 2 weeks. The median weight of protein substitute (with or without vitamin and mineral supplements) consumed decreased by 33% from 150 g (range 140-180) daily to 100 g (range 100-125) daily ( p

UR - http://www.scopus.com/inward/record.url?scp=2942568160&partnerID=8YFLogxK

U2 - 10.1023/B:BOLI.0000028784.11080.9b

DO - 10.1023/B:BOLI.0000028784.11080.9b

M3 - Article

C2 - 15159643

VL - 27

SP - 127

EP - 135

JO - Journal of Inherited Metabolic Disease

JF - Journal of Inherited Metabolic Disease

SN - 0141-8955

ER -